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Epithelioid sarcoma is a peculiar form of sarcoma that has repeatedly been confused with a variety of benign and malignant diseases, especially a granulomatous process, a synovial sarcoma, or an ulcerating squamous cell carcinoma. The tumor occurs chiefly in young adults and adolescents and predominates in male. The soft tissues of the hand, the forearm, and the pretibial region are the most frequently affected sites. It tends to grow in a nodular or multinodular manner along fibrous structures such as tendons and fascia. Microscopically, the tumor consists of irregular nodular masses of large, deeply acidophilic polygonal or epithelioid cells merging with spindle cells. The tumor recurred in 85 per cent of Enzingers cases and metastasized in 30 per cent. Cure may be achieved by wide local excision at early stage of disease. Authors report a case of epithelioid sarcoma on flexor surface of right forearm. The patient was 26 year old male. The nodular walnut sized tumor was widely excised and the defect was covered with medium split thickness skin graft from thigh.
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